Metastatic esthesioneuroblastoma secreting adrenocorticotropic hormone in pediatric patients

Silvestre Galioto, Alessandro Di Petrillo, Mauro Pastori, Alberto Arecchi

Research output: Contribution to journalArticle

7 Citations (Scopus)

Abstract

The purpose of this article was to report a pediatric case of secondary cervical esthesioneuroblastoma involving the parapharyngeal lymph nodes. A 3-year-old boy came to our clinical observation because of a right lymphonodal mass evidenced by nuclear magnetic resonance and a diagnosis of Cushing syndrome associated with ectopic adrenocorticotropic hormone secretion, moon face, central obesity, asthenia, and hirsutism. At the age of 10 months, the patient underwent endoscopic surgery for asportation of the World Health Organization stage IVesthesioneuroblastoma. At 38 months of age, the patient underwent right parapharyngeal lymphadenectomy with surgical access by a double mandibulectomy. After surgery, serum ACTH, cortisolemia, and urinary excretion of cortisol were within the reference range. Blood pressure was recorded at 110/70 mm Hg. Moon face disappeared, as well as central obesity and hirsutism. Clinical report is presented together with brief review of literature.

Original languageEnglish
Pages (from-to)1924-1929
Number of pages6
JournalJournal of Craniofacial Surgery
Volume22
Issue number5
DOIs
Publication statusPublished - Sep 2011

Fingerprint

Olfactory Esthesioneuroblastoma
Hirsutism
Abdominal Obesity
Adrenocorticotropic Hormone
Ectopic Hormones
Pediatrics
Asthenia
Cushing Syndrome
Patient Rights
Lymph Node Excision
Hydrocortisone
Reference Values
Magnetic Resonance Spectroscopy
Lymph Nodes
Observation
Blood Pressure
Serum

Keywords

  • Cushing syndrome
  • Ectopic ACTH
  • Parapharyngeal lymph nodes metastasis
  • Pediatric esthesioneuroblastoma

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Surgery

Cite this

Metastatic esthesioneuroblastoma secreting adrenocorticotropic hormone in pediatric patients. / Galioto, Silvestre; Di Petrillo, Alessandro; Pastori, Mauro; Arecchi, Alberto.

In: Journal of Craniofacial Surgery, Vol. 22, No. 5, 09.2011, p. 1924-1929.

Research output: Contribution to journalArticle

Galioto, Silvestre ; Di Petrillo, Alessandro ; Pastori, Mauro ; Arecchi, Alberto. / Metastatic esthesioneuroblastoma secreting adrenocorticotropic hormone in pediatric patients. In: Journal of Craniofacial Surgery. 2011 ; Vol. 22, No. 5. pp. 1924-1929.
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