Abstract
Progressive facial hemiatrophy or Perry-Romberg syndrome is a rare entity characterized by unilateral atrophy of the skin, subcutaneous tissue, end the underlying bony structures. This syndrome has many features of linear scleroderma en coup de sabre but is distinguished by more extensive involvement of the lower face end by only slight cutaneous sclerosis. We describe two unusual children with both etrophic and sclerotic changes of half of the face coexisting with multiple plaques of typical morphea. Both children developed neurologic disturbances with cranial magnetic resonance imaging (MRI) abnormalities 2 years and 15 years, respectively, after the onset of cutaneous lesions. Thus considering that it may not be possible to correlate impairment in neurologic function and cutaneous disease, as illustrated by our patients, we emphasize the importance of an accurate follow-up.
| Original language | English |
|---|---|
| Pages (from-to) | 113-116 |
| Number of pages | 4 |
| Journal | Pediatric Dermatology |
| Volume | 14 |
| Issue number | 2 |
| Publication status | Published - 1997 |
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ASJC Scopus subject areas
- Dermatology
- Pediatrics, Perinatology, and Child Health
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Neurologic abnormalities in two patients with facial hemiatrophy and sclerosis coexisting with morphea. / Menni, Silvano; Marzano, Angelo Valerio; Passoni, Emanuela.
In: Pediatric Dermatology, Vol. 14, No. 2, 1997, p. 113-116.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Neurologic abnormalities in two patients with facial hemiatrophy and sclerosis coexisting with morphea
AU - Menni, Silvano
AU - Marzano, Angelo Valerio
AU - Passoni, Emanuela
PY - 1997
Y1 - 1997
N2 - Progressive facial hemiatrophy or Perry-Romberg syndrome is a rare entity characterized by unilateral atrophy of the skin, subcutaneous tissue, end the underlying bony structures. This syndrome has many features of linear scleroderma en coup de sabre but is distinguished by more extensive involvement of the lower face end by only slight cutaneous sclerosis. We describe two unusual children with both etrophic and sclerotic changes of half of the face coexisting with multiple plaques of typical morphea. Both children developed neurologic disturbances with cranial magnetic resonance imaging (MRI) abnormalities 2 years and 15 years, respectively, after the onset of cutaneous lesions. Thus considering that it may not be possible to correlate impairment in neurologic function and cutaneous disease, as illustrated by our patients, we emphasize the importance of an accurate follow-up.
AB - Progressive facial hemiatrophy or Perry-Romberg syndrome is a rare entity characterized by unilateral atrophy of the skin, subcutaneous tissue, end the underlying bony structures. This syndrome has many features of linear scleroderma en coup de sabre but is distinguished by more extensive involvement of the lower face end by only slight cutaneous sclerosis. We describe two unusual children with both etrophic and sclerotic changes of half of the face coexisting with multiple plaques of typical morphea. Both children developed neurologic disturbances with cranial magnetic resonance imaging (MRI) abnormalities 2 years and 15 years, respectively, after the onset of cutaneous lesions. Thus considering that it may not be possible to correlate impairment in neurologic function and cutaneous disease, as illustrated by our patients, we emphasize the importance of an accurate follow-up.
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UR - http://www.scopus.com/inward/citedby.url?scp=0031000839&partnerID=8YFLogxK
M3 - Article
C2 - 9144696
AN - SCOPUS:0031000839
VL - 14
SP - 113
EP - 116
JO - Pediatric Dermatology
JF - Pediatric Dermatology
SN - 0736-8046
IS - 2
ER -