Not all symptoms disappear after vascular ring division: A pathophysiological interpretation

Augusto Zani, Francesco Morini, Pasquale Paolantonio, Denis A. Cozzi

Research output: Contribution to journalArticlepeer-review

Abstract

Vascular rings are a group of cardiovascular lesions due to faulty embryological development derived from an abnormality of neural crest cells (cephalic neurocristopathy). In addition to peculiar symptoms due to compression on the trachea and/or the esophagus, patients with vascular rings might present further features of neural crest-related defects. We report on a case of a child with complete vascular ring, affected both by compressive symptoms and by autonomic disturbances and minor facial anomalies. The autonomic disturbances are clinical features of maturational dysautonomia and tend to disappear with aging, whereas major compressive symptoms are solved by surgery.

Original languageEnglish
Pages (from-to)676-678
Number of pages3
JournalPediatric Cardiology
Volume29
Issue number3
DOIs
Publication statusPublished - May 2008

Keywords

  • Bark cough
  • Clinical manifestation
  • Ligamentum arteriosum
  • Maturational dysautonomia
  • Neural crest
  • Vascular ring

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pediatrics, Perinatology, and Child Health

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