Orthodontic treatment in a patient with cleidocranial dysostosis

Giampietro Farronato, Cinzia Maspero, Davide Farronato, Silvia Gioventù

Research output: Contribution to journalArticle

Abstract

Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with clavicular hypoplasia or aplasia, delayed closure of cranial fontanels, brachycephalic skull, delayed exfoliation of primary dentition, eruption of permanent teeth, and multiple supernumerary and morphologic abnormalities of the maxilla and mandible. The disorder is caused by mutation in the CBFAI gene, on the short arm of chromosome 6p21. The prevalence of cleidocranial dysostosis is estimated one per million, without sex or ethnic group predilection. The purpose of this paper is to describe the orthodontic treatment in a patient with cleidocranial dysostosis. Therapy may include removal of supernumerary teeth, surgical exposure of impacted teeth, and orthodontic treatment.

Original languageEnglish
Pages (from-to)178-185
Number of pages8
JournalAngle Orthodontist
Volume79
Issue number1
DOIs
Publication statusPublished - Jan 2009

Keywords

  • Cleidocranial dysostosis
  • Hypoplastic or aplastic clavicles
  • Supernumerary teeth

ASJC Scopus subject areas

  • Orthodontics

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