Papular mucinosis associated with generalized morphoea

F. Rongioletti, P. Rampini, A. Parodi, A. Rebora

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

A 67-year-old white man is described who had large sclerotic plaques with a violaceous border on his back and abdomen and a scleroderma-like induration on the legs, sparing the feet. Additionally, he had multiple skin- coloured, large, sometimes centrally depressed papules and nodules on the nape of the neck, back and upper limbs. These occurred in both the normal and sclerotic areas. Histologically, large amounts of focal mucin were seen in the upper dermis consistent with the diagnosis of papular mucinosis and associated with typical underlying features of scleroderma. No paraproteinaemia was found. We excluded scleromyxoedema on clinical, histopathological and laboratory grounds and diagnosed our patient as having generalized morphoea with papular mucinosis. We are aware of only two reports of large cutaneous deposits of mucin associated with scleroderma.

Original languageEnglish
Pages (from-to)905-908
Number of pages4
JournalBritish Journal of Dermatology
Volume141
Issue number5
DOIs
Publication statusPublished - 1999

Fingerprint

Scleromyxedema
Localized Scleroderma
Mucins
Skin
Paraproteinemias
Dermis
Upper Extremity
Abdomen
Foot
Leg
Neck

Keywords

  • Mucin
  • Papular mucinosis
  • Scleroderma

ASJC Scopus subject areas

  • Dermatology

Cite this

Papular mucinosis associated with generalized morphoea. / Rongioletti, F.; Rampini, P.; Parodi, A.; Rebora, A.

In: British Journal of Dermatology, Vol. 141, No. 5, 1999, p. 905-908.

Research output: Contribution to journalArticle

Rongioletti, F. ; Rampini, P. ; Parodi, A. ; Rebora, A. / Papular mucinosis associated with generalized morphoea. In: British Journal of Dermatology. 1999 ; Vol. 141, No. 5. pp. 905-908.
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