Papular xanthoma associated with angiokeratoma of fordyce

Considerations on the nosography of this rare non-langerhans cell histiocytoxanthomatosis

Ruggero Caputo, Emanuela Passoni, Stefano Cavicchini

Research output: Contribution to journalArticle

8 Citations (Scopus)

Abstract

Background: Papular xanthoma (PX) is a rare normolipidemic non-Langerhans cell histiocytoxanthomatosis affecting both children and adults. Objective: We describe an adult case of PX associated with angiokeratoma of Fordyce and review the literature in order to compare and discuss previous reports. Methods: We studied the clinical, histopathological, immunocytochemical and ultrastructural findings. Results: We report the findings of our case and compare our case with those described in the literature. Conclusions: Three clinical patterns of PX appeared to emerge in the review of the literature: a self-healing form, a persistent form and a progressive form. The progressive form of PX can be considered the same clinical entity that is also described as progressive nodular histiocytosis.

Original languageEnglish
Pages (from-to)165-168
Number of pages4
JournalDermatology
Volume206
Issue number2
DOIs
Publication statusPublished - 2003

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Angiokeratoma
Xanthomatosis
Histiocytosis

Keywords

  • Non-Langerhans cell histiocytoxanthomatosis
  • Papular xanthoma
  • Progressive nodular histiocytosis

ASJC Scopus subject areas

  • Dermatology

Cite this

Papular xanthoma associated with angiokeratoma of fordyce : Considerations on the nosography of this rare non-langerhans cell histiocytoxanthomatosis. / Caputo, Ruggero; Passoni, Emanuela; Cavicchini, Stefano.

In: Dermatology, Vol. 206, No. 2, 2003, p. 165-168.

Research output: Contribution to journalArticle

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