Abstract
Mortality rates for deaths 'due to' and 'with' hereditary ataxias are presented for the first time. Age-adjusted mortality rates were higher for whites than for nonwhites of either sex, and for men in both racial groups. Age-specific mortality rates for whites showed a peak for 'hereditary spinal ataxia' in the 20-29 age group. For the other types of ataxias they were low until age 40 and increased thereafter. Heart diseases were a frequent cause of death in people dying 'with' hereditary ataxias. The median survival (from birth) for hereditary spinal ataxia in whites was 35 years.
Original language | English |
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Pages (from-to) | 193-199 |
Number of pages | 7 |
Journal | Neuroepidemiology |
Volume | 8 |
Issue number | 4 |
DOIs | |
Publication status | Published - 1989 |
Keywords
- Friedreich’s disease
- Hereditary ataxias
- Mortality
ASJC Scopus subject areas
- Epidemiology
- Clinical Neurology