Patterns of mortality from hereditary ataxias in the United States, 1971 and 1973-1978

Maurizio Leone; Vijay Chandra; Bruce S. Schoenberg

doi:10.1159/000110182

Patterns of mortality from hereditary ataxias in the United States, 1971 and 1973-1978

Maurizio Leone, Vijay Chandra, Bruce S. Schoenberg

IRCCS Casa Sollievo della Sofferenza

Research output: Contribution to journal › Article › peer-review

Abstract

Mortality rates for deaths 'due to' and 'with' hereditary ataxias are presented for the first time. Age-adjusted mortality rates were higher for whites than for nonwhites of either sex, and for men in both racial groups. Age-specific mortality rates for whites showed a peak for 'hereditary spinal ataxia' in the 20-29 age group. For the other types of ataxias they were low until age 40 and increased thereafter. Heart diseases were a frequent cause of death in people dying 'with' hereditary ataxias. The median survival (from birth) for hereditary spinal ataxia in whites was 35 years.

Original language	English
Pages (from-to)	193-199
Number of pages	7
Journal	Neuroepidemiology
Volume	8
Issue number	4
DOIs	https://doi.org/10.1159/000110182
Publication status	Published - 1989

Keywords

Friedreich’s disease
Hereditary ataxias
Mortality

ASJC Scopus subject areas

Epidemiology
Clinical Neurology

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AB - Mortality rates for deaths 'due to' and 'with' hereditary ataxias are presented for the first time. Age-adjusted mortality rates were higher for whites than for nonwhites of either sex, and for men in both racial groups. Age-specific mortality rates for whites showed a peak for 'hereditary spinal ataxia' in the 20-29 age group. For the other types of ataxias they were low until age 40 and increased thereafter. Heart diseases were a frequent cause of death in people dying 'with' hereditary ataxias. The median survival (from birth) for hereditary spinal ataxia in whites was 35 years.

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Patterns of mortality from hereditary ataxias in the United States, 1971 and 1973-1978

Abstract

Keywords

ASJC Scopus subject areas

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