Abstract
Primitive intraneural synovial sarcomas are rare in children. The authors report the case of a 7-year-old girl affected by intraneural synovial sarcoma of a lumbar nerve root, the first such lesion in this location described in a child. The lesion mimicked a schwannoma clinically and radiologically. There was long-lasting leg pain in a radicular distribution, and a well-demarcated intraneural tumor was seen on MRI. On this basis, the first resection was conservative. However, histological examination documented a classic biphasic synovial sarcoma, which was confirmed by immunohistochemistry. After radical resection and adjuvant treatment, complete disease control was achieved and verified at 5-year follow-up. This case strongly suggests that early diagnosis and a multidisciplinary approach to this unusual spinal lesion are essential to achieving a better prognosis.
Original language | English |
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Pages (from-to) | 473-477 |
Number of pages | 5 |
Journal | Journal of Neurosurgery: Pediatrics |
Volume | 11 |
Issue number | 4 |
DOIs | |
Publication status | Published - Apr 2013 |
Keywords
- Children
- Intraneural
- Nerve root
- Neurosurgery
- Oncology
- Synovial sarcoma
ASJC Scopus subject areas
- Clinical Neurology
- Surgery
- Pediatrics, Perinatology, and Child Health