TY - JOUR
T1 - Postpneumonectomy syndrome in a newborn after esophageal atresia repair
AU - Iacusso, Chiara
AU - Bagolan, Pietro
AU - Bottero, Sergio
AU - Conforti, Andrea
AU - Morini, Francesco
PY - 2015
Y1 - 2015
N2 - Introduction Postpneumonectomy syndrome (PPS) is an ominous complication, caused by mediastinal shift following massive lung resection. Presentation of the case A neonate with oesophageal atresia and tracheo-oesophageal fistula developed acute respiratory distress shortly after surgery, despite mechanical ventilation. The patient was found to have an associated oesophageal right lung that collapsed after oesophageal atresia repair and a left pulmonary artery sling causing left main bronchus stenosis mimicking a postpneumonectomy syndrome. Discussion We will describe the diagnostic work-up and the therapeutic measures used both in the acute phase and as definitive treatment in this challenging case. Conclusions Neonatologists and paediatric surgeons should be aware of this rare association that may cause acute life threatening and worsening of patient's clinical status. Prompt realignment of the mediastinum in the normal position is critical to obtain rapid improvement of the patient's clinical conditions.
AB - Introduction Postpneumonectomy syndrome (PPS) is an ominous complication, caused by mediastinal shift following massive lung resection. Presentation of the case A neonate with oesophageal atresia and tracheo-oesophageal fistula developed acute respiratory distress shortly after surgery, despite mechanical ventilation. The patient was found to have an associated oesophageal right lung that collapsed after oesophageal atresia repair and a left pulmonary artery sling causing left main bronchus stenosis mimicking a postpneumonectomy syndrome. Discussion We will describe the diagnostic work-up and the therapeutic measures used both in the acute phase and as definitive treatment in this challenging case. Conclusions Neonatologists and paediatric surgeons should be aware of this rare association that may cause acute life threatening and worsening of patient's clinical status. Prompt realignment of the mediastinum in the normal position is critical to obtain rapid improvement of the patient's clinical conditions.
KW - Communicating bronchopulmonary foregut malformations
KW - Iatrogenic hydrothorax
KW - Oesophageal atresia
KW - Oesophageal lung
KW - Postpneumonectomy syndrome
KW - Pseudo-postpneumonectomy syndrome
KW - Tissue expander
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U2 - 10.1016/j.ijscr.2015.03.047
DO - 10.1016/j.ijscr.2015.03.047
M3 - Article
AN - SCOPUS:84926004077
VL - 10
SP - 142
EP - 145
JO - International Journal of Surgery Case Reports
JF - International Journal of Surgery Case Reports
SN - 2210-2612
ER -