Primitive retinal vascular abnormalities: Tumors and telangiectasias

Karl Anders Knutsson, Umberto De Benedetto, Giuseppe Querques, Claudia Del Turco, Francesco Bandello, Rosangela Lattanzio

Research output: Contribution to journalArticlepeer-review


Primitive retinal vascular abnormalities are benign conditions of the retinal circulation that comprise vascular tumors and telangiectasias. The principal vascular tumors of the retina include retinal capillary hemangioma, cavernous hemangioma of the retina, racemose hemangiomatosis of the retina and retinal vasoproliferative tumor, while primary retinal telangiectasias include Coats' disease, Leber's miliary aneurysms and idiopathic juxtafoveal telangiectasias. In most cases, these alterations result in significant visual impairment due to exudation determined by the structural abnormalities of the retinal vasculature. The aim of this review is to assess the different clinical and diagnostic features of the single pathological entities and to discuss the available treatment modalities including the onset of intravitreal antivascular endothelial growth factor therapy.

Original languageEnglish
Pages (from-to)67-77
Number of pages11
Issue number2
Publication statusPublished - Jul 2012


  • Retinal angiomatosis
  • Retinal telangiectasias
  • Retinal vascular tumors
  • Von Hippel-Lindau syndrome

ASJC Scopus subject areas

  • Ophthalmology
  • Sensory Systems


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