Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance

Francesca Santamaria, Gianluca Brancaccio, Giancarlo Parenti, Paola Francalanci, Cosimo Squitieri, Gianfranco Sebastio, Carlo Dionisi-Vici, Patrizia D'Argenio, Generoso Andria, Francesco Parisi

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Abstract

We present a case of recurrent pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance. The recurrence of the pulmonary disease provides further insight regarding the possible pathogenesis of pulmonary alveolar proteinosis and therapeutic options for this complication.

Original languageEnglish
Pages (from-to)268-272
Number of pages5
JournalJournal of Pediatrics
Volume145
Issue number2
DOIs
Publication statusPublished - Aug 2004

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Keywords

  • BAL
  • Bronchoalveolar lavage
  • EBV
  • Epstein Barr virus
  • GM-CSF
  • Granulocyte-macrophage colony-stimulating factor
  • High-resolution computed tomography
  • HRCT
  • LPI
  • Lysinuric protein intolerance
  • Nitric oxide
  • NO
  • PAP
  • PAS
  • Pulmonary alveolar proteinosis

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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