Severe Ebstein's anomaly can benefit from a small ventricular septal defect: Two cases

A. Del Pasqua, A. De Zorzi, S. P. Sanders, G. Rinelli

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Ebstein's anomaly is a rare congenital heart defect. Associated lesions are uncommon, and the mortality rates can be as high as 54% during the first month of life. Two cases of severe Ebstein's anomaly with ventricular septal defect are described. It is speculated that this rare association, allowing adequate forward pulmonary blood flow in the neonate, permitted the reported patients to survive the neonatal period, which is the most life-threatening time. The authors propose that the presence of a small ventricular septal defect can be beneficial for such patients, averting the need for surgery during early infancy when the risk is highest.

Original languageEnglish
Pages (from-to)217-219
Number of pages3
JournalPediatric Cardiology
Volume29
Issue number1
DOIs
Publication statusPublished - Jan 2008

Fingerprint

Ebstein Anomaly
Ventricular Heart Septal Defects
Congenital Heart Defects
Newborn Infant
Lung
Mortality

Keywords

  • Congenital heart disease
  • Ebstein's anomaly
  • Ventricular septal defect

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Severe Ebstein's anomaly can benefit from a small ventricular septal defect : Two cases. / Del Pasqua, A.; De Zorzi, A.; Sanders, S. P.; Rinelli, G.

In: Pediatric Cardiology, Vol. 29, No. 1, 01.2008, p. 217-219.

Research output: Contribution to journalArticle

Del Pasqua, A. ; De Zorzi, A. ; Sanders, S. P. ; Rinelli, G. / Severe Ebstein's anomaly can benefit from a small ventricular septal defect : Two cases. In: Pediatric Cardiology. 2008 ; Vol. 29, No. 1. pp. 217-219.
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