Abstract
Ebstein's anomaly is a rare congenital heart defect. Associated lesions are uncommon, and the mortality rates can be as high as 54% during the first month of life. Two cases of severe Ebstein's anomaly with ventricular septal defect are described. It is speculated that this rare association, allowing adequate forward pulmonary blood flow in the neonate, permitted the reported patients to survive the neonatal period, which is the most life-threatening time. The authors propose that the presence of a small ventricular septal defect can be beneficial for such patients, averting the need for surgery during early infancy when the risk is highest.
| Original language | English |
|---|---|
| Pages (from-to) | 217-219 |
| Number of pages | 3 |
| Journal | Pediatric Cardiology |
| Volume | 29 |
| Issue number | 1 |
| DOIs | |
| Publication status | Published - Jan 2008 |
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Keywords
- Congenital heart disease
- Ebstein's anomaly
- Ventricular septal defect
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine
- Pediatrics, Perinatology, and Child Health
Cite this
Severe Ebstein's anomaly can benefit from a small ventricular septal defect : Two cases. / Del Pasqua, A.; De Zorzi, A.; Sanders, S. P.; Rinelli, G.
In: Pediatric Cardiology, Vol. 29, No. 1, 01.2008, p. 217-219.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Severe Ebstein's anomaly can benefit from a small ventricular septal defect
T2 - Two cases
AU - Del Pasqua, A.
AU - De Zorzi, A.
AU - Sanders, S. P.
AU - Rinelli, G.
PY - 2008/1
Y1 - 2008/1
N2 - Ebstein's anomaly is a rare congenital heart defect. Associated lesions are uncommon, and the mortality rates can be as high as 54% during the first month of life. Two cases of severe Ebstein's anomaly with ventricular septal defect are described. It is speculated that this rare association, allowing adequate forward pulmonary blood flow in the neonate, permitted the reported patients to survive the neonatal period, which is the most life-threatening time. The authors propose that the presence of a small ventricular septal defect can be beneficial for such patients, averting the need for surgery during early infancy when the risk is highest.
AB - Ebstein's anomaly is a rare congenital heart defect. Associated lesions are uncommon, and the mortality rates can be as high as 54% during the first month of life. Two cases of severe Ebstein's anomaly with ventricular septal defect are described. It is speculated that this rare association, allowing adequate forward pulmonary blood flow in the neonate, permitted the reported patients to survive the neonatal period, which is the most life-threatening time. The authors propose that the presence of a small ventricular septal defect can be beneficial for such patients, averting the need for surgery during early infancy when the risk is highest.
KW - Congenital heart disease
KW - Ebstein's anomaly
KW - Ventricular septal defect
UR - http://www.scopus.com/inward/record.url?scp=38349103001&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=38349103001&partnerID=8YFLogxK
U2 - 10.1007/s00246-007-9097-8
DO - 10.1007/s00246-007-9097-8
M3 - Article
C2 - 17874154
AN - SCOPUS:38349103001
VL - 29
SP - 217
EP - 219
JO - Pediatric Cardiology
JF - Pediatric Cardiology
SN - 0172-0643
IS - 1
ER -