Severe epilepsy preceding by four months the onset of scleroderma en coup de sabre

Stefano Sartori, Giorgia Martini, Milena Calderone, Annalisa Patrizi, Giuseppe Gobbi, Francesco Zulian

Research output: Contribution to journalArticlepeer-review

Abstract

Juvenile localized scleroderma (JLS) includes several subtypes including plaque morphea, linear scleroderma and the en coup de sabre type which affects face and head. The latter variety may involve the eye and the brain with various appearance and clinical complications. We describe the case of a 6-year-old boy who presented partial complex seizures, with status epilepticus, four months before the appearance of sclerodermatous skin lesions on the face. This case report raises important questions on the pathogenesis of JLS and, particularly, on the issue whether it is a mere autoimmune condition or a neuro-cutaneous disease.

Original languageEnglish
JournalClinical and Experimental Rheumatology
Volume27
Issue number3 SUPPL. 54
Publication statusPublished - 2009

Keywords

  • Epilepsy
  • Neuroimaging
  • Scleroderma en coup de sabre

ASJC Scopus subject areas

  • Rheumatology
  • Immunology
  • Immunology and Allergy

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