Juvenile localized scleroderma (JLS) includes several subtypes including plaque morphea, linear scleroderma and the en coup de sabre type which affects face and head. The latter variety may involve the eye and the brain with various appearance and clinical complications. We describe the case of a 6-year-old boy who presented partial complex seizures, with status epilepticus, four months before the appearance of sclerodermatous skin lesions on the face. This case report raises important questions on the pathogenesis of JLS and, particularly, on the issue whether it is a mere autoimmune condition or a neuro-cutaneous disease.
|Journal||Clinical and Experimental Rheumatology|
|Issue number||3 SUPPL. 54|
|Publication status||Published - 2009|
- Scleroderma en coup de sabre
ASJC Scopus subject areas
- Immunology and Allergy