Simultaneous occurrence of pancreatoblastoma and neuroblastoma in a newborn with beckwith-wiedemann syndrome

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Abstract

Beckwith-Wiedemann syndrome is associated with an increased risk of tumors in the pediatric age. We report the case of a newborn with Beckwith-Wiedemann syndrome presenting the simultaneous occurrence of a cystic pancreatoblastoma and an adrenal neuroblastoma. Surgery was required to treat the pancreato-blastoma, and a ''wait and see'' policy was adopted for the neuro-blastoma, which spontaneously regressed within a few months.

Original languageEnglish
JournalJournal of Pediatric Hematology/Oncology
Volume32
Issue number5
DOIs
Publication statusPublished - Jul 2010

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Beckwith-Wiedemann Syndrome
Neuroblastoma
Pediatrics
Neoplasms
Pancreatoblastoma

Keywords

  • Adrenal mass
  • Beckwith-Wiedemann syndrome
  • Congenital neuroblastoma
  • Cystic pancreatoblastoma

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Oncology
  • Hematology
  • Medicine(all)

Cite this

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title = "Simultaneous occurrence of pancreatoblastoma and neuroblastoma in a newborn with beckwith-wiedemann syndrome",
abstract = "Beckwith-Wiedemann syndrome is associated with an increased risk of tumors in the pediatric age. We report the case of a newborn with Beckwith-Wiedemann syndrome presenting the simultaneous occurrence of a cystic pancreatoblastoma and an adrenal neuroblastoma. Surgery was required to treat the pancreato-blastoma, and a ''wait and see'' policy was adopted for the neuro-blastoma, which spontaneously regressed within a few months.",
keywords = "Adrenal mass, Beckwith-Wiedemann syndrome, Congenital neuroblastoma, Cystic pancreatoblastoma",
author = "Stefania Sorrentino and Massimo Conte and Paolo Nozza and Claudio Granata and Valeria Capra and Stefano Avanzini and Alberto Garaventa",
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T1 - Simultaneous occurrence of pancreatoblastoma and neuroblastoma in a newborn with beckwith-wiedemann syndrome

AU - Sorrentino, Stefania

AU - Conte, Massimo

AU - Nozza, Paolo

AU - Granata, Claudio

AU - Capra, Valeria

AU - Avanzini, Stefano

AU - Garaventa, Alberto

PY - 2010/7

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N2 - Beckwith-Wiedemann syndrome is associated with an increased risk of tumors in the pediatric age. We report the case of a newborn with Beckwith-Wiedemann syndrome presenting the simultaneous occurrence of a cystic pancreatoblastoma and an adrenal neuroblastoma. Surgery was required to treat the pancreato-blastoma, and a ''wait and see'' policy was adopted for the neuro-blastoma, which spontaneously regressed within a few months.

AB - Beckwith-Wiedemann syndrome is associated with an increased risk of tumors in the pediatric age. We report the case of a newborn with Beckwith-Wiedemann syndrome presenting the simultaneous occurrence of a cystic pancreatoblastoma and an adrenal neuroblastoma. Surgery was required to treat the pancreato-blastoma, and a ''wait and see'' policy was adopted for the neuro-blastoma, which spontaneously regressed within a few months.

KW - Adrenal mass

KW - Beckwith-Wiedemann syndrome

KW - Congenital neuroblastoma

KW - Cystic pancreatoblastoma

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