TY - JOUR
T1 - Sudden death in an infant revealing atypical Kawasaki disease
AU - Diana, Maria Cristina
AU - Villa, Giovanna
AU - Gattorno, Marco
AU - Ottonello, Giancarlo
AU - Costabel, Simona
AU - Savioli, Cesarina
AU - DiPietro, Pasquale
PY - 2006/1
Y1 - 2006/1
N2 - We present a case of a 4-month-old girl referred to the emergency department with a provisional diagnosis of acute life-threatening event with a recent episode of heart block and a history of long-lasting fever. Soon after admission, the child suddenly deteriorated rapidly; she became pulseless with complete heart block and died despite intensive resuscitation efforts. Postmortem examination showed coronary arteritis with aneurysmal dilatation and coronary thrombosis, revealing atypical Kawasaki disease. With this case presentation, we discuss the importance of early recognition and treatment of atypical and/or incomplete forms of Kawasaki disease, which are most common in young infants and may lead, if untreated, to coronary artery abnormalities with a potential for myocardial infarctions, aneurysm formation, and sudden death. In addition, the relevance of postmortem examination in a case of sudden and undiagnosed infant death is underlined.
AB - We present a case of a 4-month-old girl referred to the emergency department with a provisional diagnosis of acute life-threatening event with a recent episode of heart block and a history of long-lasting fever. Soon after admission, the child suddenly deteriorated rapidly; she became pulseless with complete heart block and died despite intensive resuscitation efforts. Postmortem examination showed coronary arteritis with aneurysmal dilatation and coronary thrombosis, revealing atypical Kawasaki disease. With this case presentation, we discuss the importance of early recognition and treatment of atypical and/or incomplete forms of Kawasaki disease, which are most common in young infants and may lead, if untreated, to coronary artery abnormalities with a potential for myocardial infarctions, aneurysm formation, and sudden death. In addition, the relevance of postmortem examination in a case of sudden and undiagnosed infant death is underlined.
KW - Acute life-threatening event
KW - Kawasaki disease
KW - Sudden infant death
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U2 - 10.1097/01.pec.0000195757.74328.68
DO - 10.1097/01.pec.0000195757.74328.68
M3 - Article
C2 - 16418610
AN - SCOPUS:31144440836
VL - 22
SP - 35
EP - 37
JO - Pediatric Emergency Care
JF - Pediatric Emergency Care
SN - 0749-5161
IS - 1
ER -