La stenosi sopravalvolare aortica. Analisi di una serie chirurgica di 8 pazienti.

Translated title of the contribution: Supravalvular aortic stenosis. Analysis of a surgical series of 8 patients

L. Zannini, R. Galli, G. Gargiulo, M. C. Santorelli, M. Nastasi, A. Pierangeli

Research output: Contribution to journalArticle

Abstract

Supravalvular aortic stenosis (SAS) is an unusual form of progressive left ventricular outflow tract (LVOT) obstruction, frequently associated with others vascular and physical anomalies. Between July 1980 and July 1986 eight such patients have been operated upon. In seven patients patch aortoplasty (according to McGoon or Doty technique) relieved the stenosis; in one, a two years old boy, with associated severe hypoplasia of the ascending aorta and aortic arch, a left ventricle (LV) - abdominal aorta valved conduit was associated to aortoplasty. One patient died in the operating room with a severe anterior myocardial infarction; seven patients are in good clinical condition at a mean follow-up of 32 months. The aortic supravalvular gradient was dramatically reduced in all patients according with Doppler echocardiography. In our mind, patients with SAS would benefit from an early surgical repair, because of progressive involvement of the aortic valve, coronary arteries and LV. The surgical technique is strictly related to the anatomical situations. Per and postoperative management should rely on the pathophysiology peculiar to this malformation (especially about coronary perfusion). Taking care to these points, the surgical results at a mid term follow-up are now very satisfactory in this cardiac malformation.

Translated title of the contributionSupravalvular aortic stenosis. Analysis of a surgical series of 8 patients
Original languageItalian
Pages (from-to)1045-1049
Number of pages5
JournalGiornale Italiano di Cardiologia
Volume17
Issue number12
Publication statusPublished - Dec 1987

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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    Zannini, L., Galli, R., Gargiulo, G., Santorelli, M. C., Nastasi, M., & Pierangeli, A. (1987). La stenosi sopravalvolare aortica. Analisi di una serie chirurgica di 8 pazienti. Giornale Italiano di Cardiologia, 17(12), 1045-1049.