Surgical outcome of partial Shone complex

Antonio Grimaldi, Anna Chiara Vermi, Siew Yen Ho, Federico Pappalardo, Alessandro Castiglioni, Stefano Benussi, Alberto Zangrillo, Ottavio Alfieri

Research output: Contribution to journalArticle

Abstract

Partial forms of Shone complex are rare. Surgical outcomes of the complete forms have generally been poor, whereas there is a lack of data on long-term follow-up of surgically treated adult partial complex. Between 2001 and 2011, nine patients (age: 38 ± 8 years; six males, 67%) were referred for valvular heart disease. Transthoracic and transoesophageal echocardiography was performed. Data were confirmed by intra-operative findings and reports. Patients were diagnosed as partial Shone complex and presented with mitral stenosis (MS) (45%) or mitral regurgitation (22%) or aortic regurgitation (22%). All but one patient (89%) reported previous surgery: coarctation of the aorta repair (87.5%) and aortic valvulotomy (12.5%). Redo intervention included: mitral valve replacement (25%), mitral repair (25%), aortic valve replacement (37.5%) and subvalvular aortic ridge resection (25%). One patient refused surgery. Patients surgically treated before the age of 5 (87.5%) showed favourable outcome (survival rate: 100%) and a 23.6 (± 4.6)-year follow-up free from events. The patient who underwent first intervention at the age of 50 and the patient with MS who refused surgery showed a 45 (± 7)-year follow-up free from major morbidity. Patients with partial Shone complex, properly diagnosed and treated, show favourable surgical outcome free from major clinical events.

Original languageEnglish
Pages (from-to)440-444
Number of pages5
JournalInteractive Cardiovascular and Thoracic Surgery
Volume14
Issue number4
DOIs
Publication statusPublished - Apr 2012

Keywords

  • Aortic coarctation
  • Congenital heart disease
  • Parachute mitral valve
  • Shone's syndrome

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pulmonary and Respiratory Medicine
  • Surgery

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