Surgical treatment of congenital rhabdoid tumor in a 10-day-old newborn

Valerio Ramieri, Emanuela Basile, Nikhil Carlo Cascone, Paolo Arangio, Claudio Ungari, Paolo Gennaro, Andrea Di Cataldo, Angela Sementa, Mario Giuseppe Romeo, Anna Clerico, Milena La Spina, Salvatore DAmico, Maria Licciardello, Pietro Milone, Piero Cascone

Research output: Contribution to journalArticle

Abstract

Background: Malignant rhabdoid tumors are rare and aggressive tumors of pediatric age. The primary tumor can occur in different localizations, but it mainly involves kidney, soft tissue, or central nervous system. It has been associated to a poor diagnosis. Methods: The authors present the case of a 10-day-old newborn affected by a bulky nasofronto-orbitary neoplasm. The patient underwent radical surgical treatment and further excision of a preauricular metastasis combined with postoperative chemotherapy treatment. Results: The authors adopted a diagnostic and therapeutic protocol according to international guidelines, not without difficulty because the first histological report showed esthesioneuroblastoma. The rarity and aggresivity of rhabdoid tumor and the precocity of onset in our patient presented a difficulty to define prognostic factors and survival rates, as well as therapeutic plan of treatment. Conclusions: The authors underline the importance of a correct prenatal diagnosis and an early surgical treatment to reach the complete healing of the patient.

Original languageEnglish
Pages (from-to)523-525
Number of pages3
JournalJournal of Craniofacial Surgery
Volume24
Issue number2
DOIs
Publication statusPublished - Mar 2013

Keywords

  • Congenital tumor
  • Malignant rhabdoid tumor
  • Surgical treatment of rhabdoid tumor

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Surgery

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  • Cite this

    Ramieri, V., Basile, E., Cascone, N. C., Arangio, P., Ungari, C., Gennaro, P., Di Cataldo, A., Sementa, A., Romeo, M. G., Clerico, A., La Spina, M., DAmico, S., Licciardello, M., Milone, P., & Cascone, P. (2013). Surgical treatment of congenital rhabdoid tumor in a 10-day-old newborn. Journal of Craniofacial Surgery, 24(2), 523-525. https://doi.org/10.1097/SCS.0b013e31828043bd