TY - CHAP
T1 - The burden of rare cancers in europe
AU - Gatta, Gemma
AU - Capocaccia, Riccardo
AU - Trama, Annalisa
AU - Martínez-García, Carmen
PY - 2010
Y1 - 2010
N2 - The burden of rare tumors in Europe is still unknown and no generally accepted definition of them exist. The Surveillance of Rare Cancers in Europe project (funded by the European Commission) aimed at providing a definition of "rare cancer", a list of cancers and rare cancer burden indicators, based on population-based cancer registry data, across Europe. An international consensus group agreed that incidence is the most appropriate indicator for measuring rare cancers frequency and set the threshold for rarity at 6/100,000/year. The list of rare cancers was based on the International Classification of Diseases for Oncology (ICD-O 3rd edition) and it was hierarchically structured in 2 layers based on various combinations of ICD-O morphology and topography codes: Layer (1) families of tumors (relevant for the health care organisation) and layer (2) tumors clinically meaningful (relevant for clinical decision making and research). The burden indicators were estimated and are provided in this chapter.
AB - The burden of rare tumors in Europe is still unknown and no generally accepted definition of them exist. The Surveillance of Rare Cancers in Europe project (funded by the European Commission) aimed at providing a definition of "rare cancer", a list of cancers and rare cancer burden indicators, based on population-based cancer registry data, across Europe. An international consensus group agreed that incidence is the most appropriate indicator for measuring rare cancers frequency and set the threshold for rarity at 6/100,000/year. The list of rare cancers was based on the International Classification of Diseases for Oncology (ICD-O 3rd edition) and it was hierarchically structured in 2 layers based on various combinations of ICD-O morphology and topography codes: Layer (1) families of tumors (relevant for the health care organisation) and layer (2) tumors clinically meaningful (relevant for clinical decision making and research). The burden indicators were estimated and are provided in this chapter.
KW - Incidence
KW - Population based cancer registry
KW - Prevalence
KW - Rare tumor
KW - Survival
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U2 - 10.1007/978-90-481-9485-8_17
DO - 10.1007/978-90-481-9485-8_17
M3 - Chapter
C2 - 20824452
AN - SCOPUS:79952048888
SN - 9789048194841
VL - 686
T3 - Advances in Experimental Medicine and Biology
SP - 285
EP - 303
BT - Advances in Experimental Medicine and Biology
ER -