The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis

M. Luisetti, R. Fiocca, E. Pozzi, V. De Rose, U. Magrini, C. Grassi

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

Approximately 200 cases of Hermansky-Pudlak syndrome have so far been reported in the literature; lung involvement is infrequent and consists in diffuse interstitial pulmonary fibrosis, which is progressive and responds poorly to corticosteroids. The disease is especially common among Puerto Ricans and, to lesser extent, in North Europeans; to the authors' knowledge, this is the first report of a patient from the Mediterranean area.

Original languageEnglish
Pages (from-to)301-305
Number of pages5
JournalEuropean Journal of Respiratory Diseases
Volume68
Issue number4
Publication statusPublished - 1986

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Hermanski-Pudlak Syndrome
Pulmonary Fibrosis
Hispanic Americans
Adrenal Cortex Hormones
Neutrophils
Macrophages
Lung

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

Cite this

Luisetti, M., Fiocca, R., Pozzi, E., De Rose, V., Magrini, U., & Grassi, C. (1986). The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis. European Journal of Respiratory Diseases, 68(4), 301-305.

The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis. / Luisetti, M.; Fiocca, R.; Pozzi, E.; De Rose, V.; Magrini, U.; Grassi, C.

In: European Journal of Respiratory Diseases, Vol. 68, No. 4, 1986, p. 301-305.

Research output: Contribution to journalArticle

Luisetti, M, Fiocca, R, Pozzi, E, De Rose, V, Magrini, U & Grassi, C 1986, 'The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis', European Journal of Respiratory Diseases, vol. 68, no. 4, pp. 301-305.
Luisetti, M. ; Fiocca, R. ; Pozzi, E. ; De Rose, V. ; Magrini, U. ; Grassi, C. / The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis. In: European Journal of Respiratory Diseases. 1986 ; Vol. 68, No. 4. pp. 301-305.
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