Abstract
Approximately 200 cases of Hermansky-Pudlak syndrome have so far been reported in the literature; lung involvement is infrequent and consists in diffuse interstitial pulmonary fibrosis, which is progressive and responds poorly to corticosteroids. The disease is especially common among Puerto Ricans and, to lesser extent, in North Europeans; to the authors' knowledge, this is the first report of a patient from the Mediterranean area.
| Original language | English |
|---|---|
| Pages (from-to) | 301-305 |
| Number of pages | 5 |
| Journal | European Journal of Respiratory Diseases |
| Volume | 68 |
| Issue number | 4 |
| Publication status | Published - 1986 |
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ASJC Scopus subject areas
- Pulmonary and Respiratory Medicine
Cite this
The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis. / Luisetti, M.; Fiocca, R.; Pozzi, E.; De Rose, V.; Magrini, U.; Grassi, C.
In: European Journal of Respiratory Diseases, Vol. 68, No. 4, 1986, p. 301-305.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - The Hermansky-Pudlak syndrome. A case with macrophage-neutrophil alveolitis
AU - Luisetti, M.
AU - Fiocca, R.
AU - Pozzi, E.
AU - De Rose, V.
AU - Magrini, U.
AU - Grassi, C.
PY - 1986
Y1 - 1986
N2 - Approximately 200 cases of Hermansky-Pudlak syndrome have so far been reported in the literature; lung involvement is infrequent and consists in diffuse interstitial pulmonary fibrosis, which is progressive and responds poorly to corticosteroids. The disease is especially common among Puerto Ricans and, to lesser extent, in North Europeans; to the authors' knowledge, this is the first report of a patient from the Mediterranean area.
AB - Approximately 200 cases of Hermansky-Pudlak syndrome have so far been reported in the literature; lung involvement is infrequent and consists in diffuse interstitial pulmonary fibrosis, which is progressive and responds poorly to corticosteroids. The disease is especially common among Puerto Ricans and, to lesser extent, in North Europeans; to the authors' knowledge, this is the first report of a patient from the Mediterranean area.
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UR - http://www.scopus.com/inward/citedby.url?scp=0022912467&partnerID=8YFLogxK
M3 - Article
C2 - 3732426
AN - SCOPUS:0022912467
VL - 68
SP - 301
EP - 305
JO - European Journal of Respiratory Diseases
JF - European Journal of Respiratory Diseases
SN - 0106-4339
IS - 4
ER -