TY - JOUR
T1 - Thoracic involvement in generalised lymphatic anomaly (or lymphangiomatosis)
AU - Luisi, Francesca
AU - Torre, Olga
AU - Harari, Sergio
PY - 2016/6/1
Y1 - 2016/6/1
N2 - Generalised lymphatic anomaly (GLA), also known as lymphangiomatosis, is a rare disease caused by congenital abnormalities of lymphatic development. It usually presents in childhood but can also be diagnosed in adults. GLA encompasses a wide spectrum of clinical manifestations ranging from singleorgan involvement to generalised disease. Given the rarity of the disease, most of the information regarding it comes from case reports. To date, no clinical trials concerning treatment are available. This review focuses on thoracic GLA and summarises possible diagnostic and therapeutic approaches.
AB - Generalised lymphatic anomaly (GLA), also known as lymphangiomatosis, is a rare disease caused by congenital abnormalities of lymphatic development. It usually presents in childhood but can also be diagnosed in adults. GLA encompasses a wide spectrum of clinical manifestations ranging from singleorgan involvement to generalised disease. Given the rarity of the disease, most of the information regarding it comes from case reports. To date, no clinical trials concerning treatment are available. This review focuses on thoracic GLA and summarises possible diagnostic and therapeutic approaches.
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U2 - 10.1183/16000617.0018-2016
DO - 10.1183/16000617.0018-2016
M3 - Review article
AN - SCOPUS:84971577838
VL - 25
SP - 170
EP - 177
JO - European Respiratory Review
JF - European Respiratory Review
SN - 0905-9180
IS - 140
ER -