Thrombotic Thrombocytopenic Purpura and Haemolytic-Uraemic Syndrome (Congenital and Acquired)

Pier M. Mannucci, Flora Peyvandi, Roberta Palla

Research output: Chapter in Book/Report/Conference proceedingChapter

Original languageEnglish
Title of host publicationPostgraduate Haematology: Sixth Edition
Number of pages12
ISBN (Print)9781405191807
Publication statusPublished - Nov 16 2010


  • Atypical (non-diarrhoea-related) HUS
  • Conditions and diseases associated with TTP
  • Congenital TTP, rare - representing 5% of all TTP cases
  • Diarrhoea-related HUS, well characterized from aetiological standpoint
  • Familial HUS - autosomal recessive and dominant forms of familial HUS - without diarrhoeal prodromes
  • Haemolytic-uraemic syndrome - form of HUS, diarrhoea-related HUS, or D(+) HUS
  • Interaction between VWF multimers of regular size - and ADAMTS-13 in plasma
  • Patients with congenital TTP - responding to plasma infusion
  • Thrombotic thrombocytopenic purpura (TTP)
  • Thrombotic thrombocytopenic purpura and haemolytic-uraemic syndrome - congenital and acquired

ASJC Scopus subject areas

  • Medicine(all)

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