Vulvar " proximal-type" epithelioid sarcoma: Report of a case and review of the literature

Lodovico Patrizi, Giacomo Corrado, Maria Saltari, Letizia Perracchio, Chiara Scelzo, Emilio Piccione, Enrico Vizza

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Background: The " proximal-type" epithelioid sarcoma is a very rare kind of mesenchimal tumor characterized by the difficulty in histological diagnosis and the very aggressive biological behavior.Case: We report of a case of a 63 years old woman with a vulvar " proximal-type" epithelioid sarcoma that underwent a radical surgical staging followed by an adjuvant radiotherapy. She is on follow-up care for 14 months and there is no clinical evidence of disease.Conclusion: Even if quite rare the proximal type epithelioid sarcoma should be regarded as a separate entity of particularly aggressive biologic behaviour. Its diagnosis attracts controversies and criticism related to the surgical approach and the choice of an adjuvant therapy.Virtual slides: The virtual slide(s) for this article can be found here:

Original languageEnglish
Article number122
Pages (from-to)1-6
Number of pages6
JournalDiagnostic Pathology
Issue number1
Publication statusPublished - Jul 25 2013


  • Radical vulvectomy
  • Vulvar " proximal-type" epithelioid sarcoma
  • Vulvar cancer

ASJC Scopus subject areas

  • Histology
  • Pathology and Forensic Medicine


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