Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines

Research output: Contribution to journalArticle

24 Citations (Scopus)

Abstract

Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.

Original languageEnglish
Pages (from-to)162-167
Number of pages6
JournalPediatric Dermatology
Volume24
Issue number2
DOIs
Publication statusPublished - Mar 2007

Fingerprint

Nevus
Skin
Extremities
Porokeratosis
Hamartoma
Spine
Biopsy
Epidermal Nevus

ASJC Scopus subject areas

  • Dermatology
  • Pediatrics, Perinatology, and Child Health

Cite this

Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines. / Cambiaghi, Stefano; Gianotti, Raffaele; Caputo, Ruggero.

In: Pediatric Dermatology, Vol. 24, No. 2, 03.2007, p. 162-167.

Research output: Contribution to journalArticle

@article{2c1167dda4fb44cf8f9a6085773f29a9,
title = "Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines",
abstract = "Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.",
author = "Stefano Cambiaghi and Raffaele Gianotti and Ruggero Caputo",
year = "2007",
month = "3",
doi = "10.1111/j.1525-1470.2007.00367.x",
language = "English",
volume = "24",
pages = "162--167",
journal = "Pediatric Dermatology",
issn = "0736-8046",
publisher = "Wiley-Blackwell",
number = "2",

}

TY - JOUR

T1 - Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines

AU - Cambiaghi, Stefano

AU - Gianotti, Raffaele

AU - Caputo, Ruggero

PY - 2007/3

Y1 - 2007/3

N2 - Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.

AB - Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.

UR - http://www.scopus.com/inward/record.url?scp=33947637876&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=33947637876&partnerID=8YFLogxK

U2 - 10.1111/j.1525-1470.2007.00367.x

DO - 10.1111/j.1525-1470.2007.00367.x

M3 - Article

C2 - 17461816

AN - SCOPUS:33947637876

VL - 24

SP - 162

EP - 167

JO - Pediatric Dermatology

JF - Pediatric Dermatology

SN - 0736-8046

IS - 2

ER -