Abstract
Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.
| Original language | English |
|---|---|
| Pages (from-to) | 162-167 |
| Number of pages | 6 |
| Journal | Pediatric Dermatology |
| Volume | 24 |
| Issue number | 2 |
| DOIs | |
| Publication status | Published - Mar 2007 |
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ASJC Scopus subject areas
- Dermatology
- Pediatrics, Perinatology, and Child Health
Cite this
Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines. / Cambiaghi, Stefano; Gianotti, Raffaele; Caputo, Ruggero.
In: Pediatric Dermatology, Vol. 24, No. 2, 03.2007, p. 162-167.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Widespread porokeratotic eccrine ostial and dermal duct nevus along Blaschko lines
AU - Cambiaghi, Stefano
AU - Gianotti, Raffaele
AU - Caputo, Ruggero
PY - 2007/3
Y1 - 2007/3
N2 - Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.
AB - Porokeratotic eccrine ostial and dermal duct nevus is a congenital hamartoma of possible eccrine origin with no malignant potential. It is usually localized at the extremity of a single limb, while wider systematized distribution has rarely been documented. A child with an unusually widespread nevus following Blaschko lines is reported. The disorder had a striking presentation in the form of a systematized linear epidermal nevus composed of multiple tiny filiform keratotic spines, which histologically corresponded to columns of porokeratosis. Serial histopathologic sections of a 4-mm punch biopsy specimen barely demonstrated an anatomic relationship between the porokeratotic columns and the underlying acrosyringeal duct. This report provides further evidence of porokeratotic eccrine ostial and dermal duct nevus being distributed along Blaschko lines, thus confirming it is a peculiar epidermal nevus due to a mosaic cutaneous condition.
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UR - http://www.scopus.com/inward/citedby.url?scp=33947637876&partnerID=8YFLogxK
U2 - 10.1111/j.1525-1470.2007.00367.x
DO - 10.1111/j.1525-1470.2007.00367.x
M3 - Article
C2 - 17461816
AN - SCOPUS:33947637876
VL - 24
SP - 162
EP - 167
JO - Pediatric Dermatology
JF - Pediatric Dermatology
SN - 0736-8046
IS - 2
ER -