X-linked bulbo-spinal neuronopathy of late onset

P. Martinelli, R. Fabbri, A. S. Gabellini, E. Govoni, E. Lugaresi

Research output: Contribution to journalArticlepeer-review


Two cases of X-linked bulbo-spinal neuronopathy (BSN) of late onset are presented. An extensive review of the literature shows that, in addition to the signs of a chronic degeneration of brainstem and spinal neurons, other clinical features may also be present at the onset of the disease, or develop during its course. Some clinical, electrophysiological and anatomical data support the hypothesis that BSN is not purely a motoneuronopathy but also concerns sensory nerve.

Original languageEnglish
Pages (from-to)498-503
Number of pages6
JournalActa Neurologica Scandinavica
Issue number6
Publication statusPublished - 1985

ASJC Scopus subject areas

  • Clinical Neurology
  • Neuroscience(all)


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